Identifying and managing pulmonary arterial hypertension
Pulmonary arterial hypertension (PAH) may lead to increased pulmonary vascular resistance, compromised vasoreactivity, right heart failure, and death. PAH, a subset of pulmonary hypertension (PH), classically is associated with systemic sclerosis but also occurs with other rheumatologic conditions. Early diagnostic strategies are essential. The symptoms of PAH often are nonspecific; the most common presenting symptom is dyspnea.